Keywords

fatigue, pulmonary arterial hypertension, pulmonary hypertension, pulmonary vasodilator medications, right ventricle, transplant

Authors

1. Leeper, Barbara MN, RN-BC, CNS M-S, CCRN, FAHA
2. Powell, Brook BSN, RN, CCRN

Abstract

Abstract: Pulmonary arterial hypertension is a rare and progressive disease associated with high pulmonary vascular pressures leading to right ventricular failure and death. The exact incidence is unknown. This article provides a broad overview of the disease, including pathophysiology, risk factors, management guidelines, and pharmacologic therapies. Nursing considerations are discussed, with an emphasis on the continuum of care.